Duodenal obstruction due to annular pancreas during the neonatal period

Keywords: Pancreas, Duodenal obstruction, Congenital abnormalities, Newborn, Vomiting, Weight loss

Abstract

Introduction. Annular pancreas is an infrequent birth defect characterized by a ring of pancreatic tissue that surrounds the descending part of the duodenum. It accounts for 1 % of neonatal intestinal obstructions worldwide. Diagnosis and final treatment is surgical. The objective is to describe a neonatal clinical case with annual pancreas based on a brief literature review on its diagnosis, evolution and treatment. Case Report. Female patient, 24 days old with emetic episodes starting on the second day of life, associated with loss of weight and hydroelectrolytic instability, who was admitted to the neonatal intensive care unit for management purposes. Given the persistence of the gastrointestinal symptoms and hemodynamic instability, despite the treatment in place, and high level of suspicion of intestinal obstruction, radiology exam of upper digestive tract was performed with contrast medium, finding evidence of signs of duodenal stenosis. Laparotomy was performed, finding evidence of dilation of the second and third parts of the duodenum, thickened walls, crossed by a pancreas segment that fully occludes the light, consistent with annual pancreas. Discussion. Take the above into consideration during differential diagnoses of duodenal obstructions, given that the patient’s symptoms, as evidenced in the patient, change depending on the type of obstruction. Imaging methods must be requested to assess radiological signs, in order to clarify the diagnosis and prevent delays in the final diagnosis of annual pancreas, which is performed by means of surgical intervention. Conclusions. Annual pancreas continues to be a diagnostic challenge due to its infrequency. People suffering from this, experience variable and non-specific symptoms; more frequently vomiting, which, in this specific case, was the initial symptom. It is important to learn about the obstructive duodenal pathology, because it is one of the differential diagnoses, and thereby prevents delays in the surgical and diagnostic approach.

Author Biographies

Yury Vanessa Ortiz-Hernández, Universidad Autónoma de Bucaramanga

Médico, Universidad Autónoma de Bucaramanga, Médico de Unidad Cuidados Intensivos de la Clínica
San Luis para la mujer y el niño, Bucaramanga, Santander, Colombia

Hugo Hernán Ferreira-Traslaviña, Universidad del Rosario

Médico, Especialista en Radiología Pediátrica, Universidad del Rosario, Director Departamento de
Radiología, Clínica San Luis para la mujer y el niño, Bucaramanga, Santander, Colombia.

Luis Mauricio Duarte-Vergara, Universidad Pontificia Javeriana

Médico Cirujano, Universidad Pontificia Javeriana, Especialista en Cirugía Pediátrica del Instituto
Pediátrico Leningrado, San Petersburgo, Rusia. Cirujano Pediatra del Departamento de Cirugía de la
Clínica San Luis para la mujer y el niño, Bucaramanga, Santander, Colombia

Martha Lucia Africano-León, Universidad Pontificia Javeriana

Médico Cirujano, Universidad Pontificia Javeriana, Especialista en Pediatría Universidad Colegio Mayor
Nuestra Señora del Rosario, Especialista en Neonatología de la Universidad Militar Nueva Granada,
Profesor de cátedra de la Universidad Industrial de Santander, Coordinadora de Unidad Cuidados
Intensivos de la Clínica San Luis para la mujer y el niño, Bucaramanga, Santander, Colombia

References

Mogollón G, Luengas P, Beltrán C, Rottermann M, Del Rio S, Cabrera L. Manejo inadecuado del páncreas anular Reporte de un caso y revisión de la literatura. CIRUPED [Internet]. 2015 [citado 29 de agosto de 2018];5(3):9-15. Recuperado a partir de: https://bit. ly/2K4XoAe

Peng C, Zhenwei Z, Jianlei C, Lulu C, Jiang P, Wnxian Z, et al. A newborn patient with both annular pancreas and Meckel’s diverticulum: A case report of an unusual association. Medicine (Baltimore). 2018;97(17):1- 5. doi: 10.1097/MD.0000000000010583

Porras H, León C, Molano H. Defectos congénitos en Risaralda. Biomedica [Internet]. 2016 [citado 29 de agosto de 2018];36(4):556-563. Recuperado a partir de: https://revistabiomedica.org/index.php/biomedica/ article/view/2771

Thukral C, Freedman S. Annular pancreas. In: Whitcomb D, Grover, editors. Uptodate. [Internet]. Waltham (MA): UpToDate Inc; 2018. [citado 29 de agosto de 2018]. Recuperado a partir de: https://www. uptodate.com/contents/annular-pancreas

Tadokoro H, Takase M, Nobukawa B. Development and congenital anomalies of the pancreas. Anat Res Int [Internet]. 2011 [citado 29 de agosto de 2018];2011:1- 7. Recuperado a partir de: https://bit.ly/2Wy739m

Ruíz S, Cuesta O, Casanova R, Rodríguez J. Estenosis duodenal por páncreas anular. Presentación de un caso esporádico. Rev Ciencias Médicas [Internet]. 2006 [citado 29 de agosto de 2018];10(1):61-70. Recuperado a partir de: https://bit.ly/2XxNtXl

Cunha J, Lima M, Jukemura J, Penteado S, Jureidini R, Patzina R, et al. Unusual Clinical Presentation of Annular Pancreas in the Adult. Pancreatology [Internet]. 2005 [citado 29 de agosto de 2018];5:81–85. Recuperado a partir de: https://bit.ly/2wGvkKW

Alahmadi R, Almuhammadi S. Annular Pancreas: A cause of gastric outlet obstruction in a 20-Year- Old Patient. Am J Case Rep. 2014;15:437–440. doi:10.12659/AJCR.891041

Reiter J, Szafranski P, Breuer O, et al. Variable phenotypic presentation of a novel FOXF1 missense mutation in a single family. Pediatric Pulmonol [Internet]. 2016 [citado 29 de agosto de 2018];51:921–927. Recuperado a partir de: https://onlinelibrary.wiley.com/ doi/abs/10.1002/ppul.23425

Zegre A, Houghton J, Carmo S, et al. Mitchell Riley syndrome: a novel mutation in RFX6 Gene, Case Report in Genetics. Hindawi. 2015;2015:1-3. doi: 10.1155/2015/937201

Mandojana F, Viscido G, Bocco M, Parodi M, Picón H, Palencia R, et al. Obstrucción duodenal por páncreas anular. Rev Argent Cirug [Internet]. 2017 [citado 29 de agosto de 2018];109 (4):202-204. Recuperado a partir de: http://dx.doi.org/10.25132/raac.v109. n4.1289.es

Lim J, Porter J, Varia H, Pettit S. Annular pancreas causing duodenal obstruction in an adult. BMJ Case Rep. 2017;2017:1-2. doi 10.1136/bcr-2017-219839

Maciel R, Reis A, Casanova J, Osório A, Oliveira T, Vasconcelos E, et al. Pâncreas anular – um caso clínico. Revista Nascer e Crescer [Internet]. 2013 [citado 29 de agosto de 2018];22(2):101-103. Recuperado a partir de: https://bit.ly/2wKFn1K

Gómez J, Meneses L, Lagos O. Páncreas anular: a propósito de un caso. Cuad. - Hosp. Clín [Internet]. 2008 [citado 29 de agosto de 2018];53(1):48-51. Recuperado a partir de: https://bit.ly/2WqJ8DV

Aravena C, Vuletin F, Parra R, Mellado C, Potin M, Zúñiga S. Caso Clínico-Radiológico. Rev. chil. Pediatr [Internet]. 2006 [citado 29 de agosto de2018];77(5):518-522. Recuperado a partir de: https:// bit.ly/2WoLp2v

Jimenez J, Emil S, Podnos Y, Nguyen N. Annular pancreas in children: A recent decade’s experience. J Pediatr Surg [Internet]. 2004 [citado 29 de agosto de 2018];39(11):1654-1657. Recuperado a partir de: https://www.sciencedirect.com/science/article/pii/ S002234680400449X

Maldonado J, Royo Y, Pueyo C, Skrabski R, Di Crosta I. Urgencias quirúrgicas en la vía digestiva. Protocolos de Neonatología. AEPED [Internet]. 2008 [citado 29 de agosto de 2018];2da edición:470–476. Recuperado a partir de: https://www.aeped.es/sites/default/files/ documentos/50.pdf

Montaño J, Arnez H, Villalpando J. Atresia de esófago con páncreas anular- caso clínico radiológico. Revista de Diagnóstico por Imágenes [Internet]. 2007 [citado 29 de agosto de 2018];2(2):21-23. Recuperado a partir de: https://bit.ly/2KEhLDZ

Uriguen M, Lozada M, Rodriguez A, Alcivar G. Diagnóstico Prenatal de Atresia duodenal por páncreas anular. Rev. Latin. Perinat [Internet]. 2017 [citado 29 de agosto de 2018];20(1):55-57. Recuperado a partir de: https://bit.ly/2ZkveoN

Escobar M, Ladd A, Grosfeld J, West K, Rescorla F, Scherer L, et al. Duodenal atresia and stenosis: longterm follow-up over 30 years. J Pediatr Surg [Internet]. 2004 [citado 29 de agosto de 2018];39(6):867– 871. Recuperado a partir de: https://www.ncbi.nlm. nih.gov/pubmed/15185215

How to Cite
1.
Ortiz-Hernández YV, Ferreira-Traslaviña HH, Duarte-Vergara LM, Africano-León ML. Duodenal obstruction due to annular pancreas during the neonatal period. MedUNAB [Internet]. 2019 Jul. 30 [cited 2026 Mar. 10];22(1):79-87. Available from: https://revistasunabeduco.biteca.online/index.php/medunab/article/view/3423

Downloads

Download data is not yet available.
Published
2019-07-30

Altmetric

Article metrics
Abstract views
Galley vies
PDF Views
HTML views
Other views
Escanea para compartir
QR Code
Crossref Cited-by logo

Some similar items: